Adenoma of the non-pigmented ciliary epithelium in a 13-year old child

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Abstract

Adenoma of the non-pigmented ciliary epithelium (NPCE) is a rare intraocular tumor which is often misinterpreted as a melanoma of the ciliary body or a non-tumorous process. We present a complex clinical, instrumental and morphological analysis of a case of adenoma of the NPCE growing into the base of the iris and the anterior chamber angle in a 13-year old child. Surgical treatment (iridocyclectomy) was performed. An adenoma of the NPCE was confirmed both histologically and by immunohistochemistry. At 6 months after surgery the patient's visual acuity was 1.0, with no signs of the tumor recurrence. The case can help to better understand clinical manifestation, results of the instrumental diagnostic assessments and the morphological picture of adenoma of NPCE that will be useful in the complex diagnosis of various intraocular tumors.

About the authors

S. V. Saakyan

Moscow Helmholtz Research Institute of Eye Diseases

Email: fake@neicon.ru

MD, PhD, Professor, Head of Department of Ophthalmic Oncology and Radiology

14/19 Sadovaya-Chernogryazskaya ul., Moscow, 105062, Russian Federation

Russian Federation

A. G. Amiryan

Moscow Helmholtz Research Institute of Eye Diseases

Author for correspondence.
Email: amiryan@yandex.ru

MD, PhD, Leading Research Fellow, Department of Ophthalmic Oncology and Radiology

14/19 Sadovaya-Chernogryazskaya ul., Moscow, 105062, Russian Federation. Tel.: +7 (495) 917 98 48

Russian Federation

I. P. Khoroshilova-Maslova

Moscow Helmholtz Research Institute of Eye Diseases

Email: fake@neicon.ru

MD, PhD, Professor, Head of Department of Pathological Anatomy and Histology

14/19 Sadovaya-Chernogryazskaya ul., Moscow, 105062, Russian Federation

Russian Federation

K. V. Lugovkina

Moscow Helmholtz Research Institute of Eye Diseases

Email: fake@neicon.ru

MD, PhD, Research Fellow, Department of Ultrasound Imaging

14/19 Sadovaya-Chernogryazskaya ul., Moscow, 105062, Russian Federation

Russian Federation

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Copyright (c) 2017 Saakyan S.V., Amiryan A.G., Khoroshilova-Maslova I.P., Lugovkina K.V.

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